The Long QT Syndrome

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45. Viskin S: Cardiac pacing in the long QT syndrome: review of available data and practical recommendations. J Cardiovasc Electrophysiol 2000;11:593-600

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50. Etheridge SP, Compton SJ, Pursley M, Kurkhardt J, Shepperd T, Mason JW: Chronic potassium shortens QTc in long QT patients with IKr defects. Pacing Clin Electrophysiol 2001;24:606(Abstract)

51. Tan HL, Alings M, Van Olden RW, Wilde AA: Long-term (subacute) potassium treatment in congenital HERG-related long QT syndrome (LQTS2). J Cardiovasc Electrophysiol 1999;10:229-233

52. Priori SG, Napolitano C, Cantu F, Brown AM, Schwartz PJ: Differential response to Na+ channel blockade, beta-adrenergic stimulation, and rapid pacing in a cellular model mimicking the SCN5A and HERG defects present in the long QT syndrome. Circ Res 1996;78:1009-1015

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54. Schwartz PJ, Priori SG, Locati EH, Napolitano C, Cantu F, Towbin JA, Keating MT, Hammoude H, Brown AM, Chen LS: Long QT syndrome patients with mutations of the SCN5A and HERG genes have differential responses to Na+ channel blockade and to increases in heart rate: implications for gene-specific therapy. Circulation 1995;92:3381-3386

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