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Hirayama Disease - A Variant of Motor Neuron Disease and Role of Flexion MRI in Diagnosis

Mahajan, SK and Kaushik, M and Raina, R and Sharath Babu, NM and Raghav, S (2013) Hirayama Disease - A Variant of Motor Neuron Disease and Role of Flexion MRI in Diagnosis. [Journal (On-line/Unpaginated)]

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Abstract

Hirayama disease is a monomyelic variant of motor neuron disease (MND) and has distinctive features of male predominance, asymmetric involvement of upper extremities with a self limiting course. Flexion MRI (magnetic resonance imaging) forms the main stay for diagnosis of this condition. Here we report such an unusual case of Hirayama disease in a male patient of 20 years who presented with weakness and atrophy in right upper limb. Careful clinical examination will help to use the flexion MRI studies for the diagnosis of this condition as done in our case.

Item Type:Journal (On-line/Unpaginated)
Keywords:Hirayama disease; Motor neuron disease; Flexion MRI; Monomyelic
Subjects:JOURNALS > Online Journal of Health and Allied Sciences
ID Code:9703
Deposited By: Kakkilaya Bevinje, Dr. Srinivas
Deposited On:21 Feb 2015 14:35
Last Modified:20 Apr 2015 11:44

References in Article

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