@misc{cogprints4278, volume = {3}, number = {3}, month = {July}, author = {Berardo Sarubbi and Pasquale Vergara and Michele D?Alto and Raffaele Calabr{\`o}}, editor = {Balbir Singh and Yash Lokhandwala and Johnson Francis and Anup Gupta}, title = {Congenital Junctional Ectopic Tachycardia: Presentation And Outcome}, publisher = {Indian Pacing and Electrophysiology Group}, year = {2003}, journal = {Indian Pacing and Electrophysiology Journal}, pages = {143--147}, keywords = {Junctional Ectopic Tachycardia, Congenital }, url = {http://cogprints.org/4278/}, abstract = {Junctional ectopic tachycardia (JET) is a rare type of supraventricular arrhythmia. Even if its management has improved in recent years, it remains a great challenge for the cardiologist. Two are the possible clinical presentations of this arrhythmia: as a primary idiopathic disorder during infancy, configuring the so called ?congenital? JET, or more often as a transient phenomenon immediately after surgery for congenital heart disease, giving rise to the ?post-operative? variety. The congenital form, firstly described as a distinct entity by Coumel et al. in 19761, usually occurs in the first six months of life presenting as a persistent sustained form, lasting up to 90\% of the time. Its clinical presentation may be dramatic, being associated in up to 60\% of cases with cardiomegaly and/or heart failure. Congenital JET is hampered by high mortality. Secondary dilated cardiomyopathy, ventricular fibrillation and sudden cardiac death have also been reported 2,3. } }