title: Congenital Junctional Ectopic Tachycardia: Presentation And Outcome creator: Sarubbi, Berardo creator: Vergara, Pasquale creator: D’Alto, Michele creator: Calabrò, Raffaele subject: Indian Pacing and Electrophysiology Journal description: Junctional ectopic tachycardia (JET) is a rare type of supraventricular arrhythmia. Even if its management has improved in recent years, it remains a great challenge for the cardiologist. Two are the possible clinical presentations of this arrhythmia: as a primary idiopathic disorder during infancy, configuring the so called “congenital” JET, or more often as a transient phenomenon immediately after surgery for congenital heart disease, giving rise to the “post-operative” variety. The congenital form, firstly described as a distinct entity by Coumel et al. in 19761, usually occurs in the first six months of life presenting as a persistent sustained form, lasting up to 90% of the time. Its clinical presentation may be dramatic, being associated in up to 60% of cases with cardiomegaly and/or heart failure. Congenital JET is hampered by high mortality. Secondary dilated cardiomyopathy, ventricular fibrillation and sudden cardiac death have also been reported 2,3. publisher: Indian Pacing and Electrophysiology Group contributor: Singh, Balbir contributor: Lokhandwala, Yash contributor: Francis, Johnson contributor: Gupta, Anup date: 2003-07 type: Journal (Paginated) type: PeerReviewed format: text/html identifier: http://cogprints.org/4278/1/sarubbi.htm identifier: Sarubbi, Berardo and Vergara, Pasquale and D’Alto, Michele and Calabrò, Raffaele (2003) Congenital Junctional Ectopic Tachycardia: Presentation And Outcome. [Journal (Paginated)] relation: http://cogprints.org/4278/