TY  - GEN
ID  - cogprints4278
UR  - http://cogprints.org/4278/
A1  - Sarubbi, Berardo
A1  - Vergara, Pasquale
A1  - D?Alto, Michele
A1  - Calabṛ, Raffaele
Y1  - 2003/07//
N2  - Junctional ectopic tachycardia (JET) is a rare type of supraventricular arrhythmia. Even if its management has improved in recent years, it remains a great challenge for the cardiologist. Two are the possible clinical presentations of this arrhythmia: as a primary idiopathic disorder during infancy, configuring the so called ?congenital? JET, or more often as a transient phenomenon immediately after surgery for congenital heart disease, giving rise to the ?post-operative? variety. 
            The congenital form, firstly described as a distinct entity by Coumel et al. in 19761, usually occurs in the first six months of life presenting as a persistent sustained form, lasting up to 90% of the time. Its clinical presentation may be dramatic, being associated in up to 60% of cases with cardiomegaly and/or heart failure. 
            Congenital JET is hampered by high mortality. Secondary dilated cardiomyopathy, ventricular fibrillation and sudden cardiac death have also been reported 2,3.
PB  - Indian Pacing and Electrophysiology Group
KW  - Junctional Ectopic Tachycardia
KW  -  Congenital 
TI  - Congenital Junctional Ectopic Tachycardia: Presentation And Outcome
SP  - 143
AV  - public
EP  - 147
ER  -