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%A Berardo Sarubbi
%A Pasquale Vergara
%A Michele D?Alto
%A Raffaele Calabr?
%J Indian Pacing and Electrophysiology Journal
%T Congenital Junctional Ectopic Tachycardia: Presentation And Outcome
%X Junctional ectopic tachycardia (JET) is a rare type of supraventricular arrhythmia. Even if its management has improved in recent years, it remains a great challenge for the cardiologist. Two are the possible clinical presentations of this arrhythmia: as a primary idiopathic disorder during infancy, configuring the so called ?congenital? JET, or more often as a transient phenomenon immediately after surgery for congenital heart disease, giving rise to the ?post-operative? variety.
The congenital form, firstly described as a distinct entity by Coumel et al. in 19761, usually occurs in the first six months of life presenting as a persistent sustained form, lasting up to 90% of the time. Its clinical presentation may be dramatic, being associated in up to 60% of cases with cardiomegaly and/or heart failure.
Congenital JET is hampered by high mortality. Secondary dilated cardiomyopathy, ventricular fibrillation and sudden cardiac death have also been reported 2,3.
%N 3
%K Junctional Ectopic Tachycardia, Congenital
%P 143-147
%E Balbir Singh
%E Yash Lokhandwala
%E Johnson Francis
%E Anup Gupta
%V 3
%D 2003
%I Indian Pacing and Electrophysiology Group
%L cogprints4278