?url_ver=Z39.88-2004&rft_val_fmt=info%3Aofi%2Ffmt%3Akev%3Amtx%3Adc&rft.title=Arrhythmogenic+Right+Ventricular+Cardiomyopathy%2FDysplasia&rft.creator=Indik%2C+Julia+H.&rft.creator=Marcus%2C+Frank+I.&rft.subject=Indian+Pacing+and+Electrophysiology+Journal&rft.description=Arrhythmogenic+right+ventricular+cardiomyopathy%2Fdysplasia+(ARVC%2FD)+is+characterized+by+the+patchy+replacement+of+myocardium+by+fatty+or+fibrofatty+tissue.+These+changes+lead+to+structural+abnormalities+including+right+ventricular+enlargement+and+wall+motion+abnormalities+that+can+be+detected+by+echocardiography%2C+angiography%2C+and+cine+MRI.+ARVC%2FD+is+a+genetically+heterogeneous+disorder%2C+since+it+has+been+linked+to+several+chromosomal+loci.+Myocarditis+may+also+be+a+contributing+etiological+factor.+Patients+are+typically+diagnosed+during+adolescence+or+young+adulthood.+Presenting+symptoms+are+generally+related+to+ventricular+arrhythmias.+Concern+for+the+risk+of+sudden+cardiac+death+may+lead+to+the+implantation+of+an+intracardiac+defibrillator.+An+ongoing+multicenter+international+registry+should+further+our+understanding+of+this+disease.%0A&rft.publisher=Indian+Pacing+and+Electrophysiology+Group&rft.contributor=Singh%2C+Balbir&rft.contributor=Lokhandwala%2C+Yash&rft.contributor=Francis%2C+Johnson&rft.contributor=Gupta%2C+Anup&rft.date=2003-07&rft.type=Journal+(Paginated)&rft.type=PeerReviewed&rft.format=text%2Fhtml&rft.identifier=http%3A%2F%2Fcogprints.org%2F4279%2F1%2Findik.htm&rft.identifier=++Indik%2C+Julia+H.+and+Marcus%2C+Frank+I.++(2003)+Arrhythmogenic+Right+Ventricular+Cardiomyopathy%2FDysplasia.++%5BJournal+(Paginated)%5D+++++&rft.relation=http%3A%2F%2Fcogprints.org%2F4279%2F