creators_name: Jagtap, SV creators_name: Nikumbh, DB creators_name: Desai, SR creators_name: Kshirsagar, AY creators_name: Khedkar, J creators_name: Chavan, SH creators_id: drdhirajnikumbh@rediffmail.com editors_name: Kakkilaya, Srinivas editors_id: BS Kakkilaya type: journale datestamp: 2012-11-09 17:37:20 lastmod: 2012-11-09 17:37:20 metadata_visibility: show title: Unusual Large Sporadic Angiomyolipoma Co-existing with Huge Simple Renal Cyst ispublished: pub subjects: OJHAS full_text_status: public keywords: Renal Angiomyolipoma; Sporadic AML; Simple renal cyst abstract: Renal Angiomyolipoma (AML) is an unusual benign mesenchymal tumor with no malignant potential. It is composed of adipose tissue, smooth muscle and abnormal thick walled blood vessels. It can occur sporadically or may be associated with tuberous sclerosis. Sporadic angiomyolipoma (AML) coexisting with simple renal cyst is extremely rare and only one case report is available in the literature. In our case, unique combination of sporadic AML along with simple renal cyst with huge size and weight was noted. To the best of our knowledge, ours is the second such case and first case from India. Due to its large size, complete nephrectomy was performed to avoid chances of rupture and retroperitoneal hemorrhage. Post-operative period was uneventful and the patient ahs been on regular follow-up. date: 2011-07-30 date_type: published publication: Online Journal of Health and Allied Sciences volume: 10 number: 2 publisher: BS Kakkilaya refereed: TRUE referencetext: 1. Steiner MS, Goldman SM, Fishman EK, Marshall FF. The natural history of renal angiomyolipoma. J Urol 1993,150:1782-86. 2. Murphy WM, Grignon DJ, Perlman EJ. Kidney tumors in adults. In Murphy WM, Grignon DJ, Perlman EJ (editor). Tumors of the Kidney, Bladder and Related Urinary Structures. AFIP. Fourth series, Fascicle 1. Washington DC, 2004. 3. Nelson CP, Sanda MG. Contemporary diagnosis and management of renal angiomyolipoma. J Urol 2002;168(1):20-24. 4. Angiomyolipoma- Kidney. [Internet] 2011. cited on 2011 March 1. Available from http://www.thedoctorsdoctor.com/diseases/kidney_angiomyolipoma.htm 5. Csata S, Repassy D, Domotor L. Co-incidence of angioleiomyolipoma and renal cyst. Acta Chir Hung.1995-96;35(3-4):355-359. 6. Jimenez RE et al. Concurrent Angiomyolipoma and Renal cell neoplasia: A study of 36 cases. Mod Pathol 2001;14:157-63. 7. Hill GS. Cystic and dysplastic disease of the kidney. In Hills GS (editor). Acquired lesions in Uropathology. Churchill Livingstone, 1st ed. 1989(1);173-88. 8. Milan JC. Tumors of the kidney. In: Hills GS (editor). Acquired lesions in Uropathology. Churchill Livingstone, 1st ed. 1989(1); 623-701. 9. Chang CC, Kuo JY, Chan WL, Chen KK, Chang LS. Prevalence and Clinical Characteristics of Simple Renal Cyst. J Chin Med Assoc. 2007;70(11):486-491. citation: Jagtap, SV and Nikumbh, DB and Desai, SR and Kshirsagar, AY and Khedkar, J and Chavan, SH (2011) Unusual Large Sporadic Angiomyolipoma Co-existing with Huge Simple Renal Cyst. [Journal (On-line/Unpaginated)] document_url: http://cogprints.org/7991/1/2011-2-29.pdf