---
abstract: 'Retinal dysplasia represents a congenital disorder characterized by abnormal proliferation of retinal tissue causing leukocoria. We present a case of an infant with bilateral leukocoria, clinically diagnosed as retinoblastoma, followed by enucleation of the left eye. Microscopy however, demonstrated retinal dysplasia consisting of a disorderly proliferation of retinal tissue with formation of rosettes, mimicking retinoblastoma. Microscopic features that aid in differentiating this lesion from retinoblastoma are discussed.'
altloc:
- http://www.ojhas.org/issue43/2012-3-10.htm
chapter: ~
commentary: ~
commref: ~
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conference: ~
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contact_email: ~
creators_id:
- drravikumar@metropolisindia.com
- ~
- ~
- ~
creators_name:
- family: Ravikumar
given: HN
honourific: ''
lineage: ''
- family: Vani
given: R
honourific: ''
lineage: ''
- family: Santosh
given: KV
honourific: ''
lineage: ''
- family: Joji
given: A
honourific: ''
lineage: ''
date: 2012-10-25
date_type: published
datestamp: 2013-05-04 23:08:39
department: ~
dir: disk0/00/00/89/20
edit_lock_since: ~
edit_lock_until: 0
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editors_id:
- Kakkilaya BS
editors_name:
- family: Kakkilaya
given: Srinivas
honourific: Dr
lineage: ''
eprint_status: archive
eprintid: 8920
fileinfo: /style/images/fileicons/application_pdf.png;/8920/1/2012-3-10.pdf
full_text_status: public
importid: ~
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isbn: ~
ispublished: pub
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keywords: Retinal Dysplasia; Retinoblastoma; Leukocoria
lastmod: 2013-05-04 23:08:39
latitude: ~
longitude: ~
metadata_visibility: show
note: ~
number: 3(10)
pagerange: ~
pubdom: TRUE
publication: Online Journal of Health and Allied Sciences
publisher: BS Kakkilaya
refereed: TRUE
referencetext: "1.\tReese AB, Blodi FC: Retinal dysplasia. Am J Ophthalmol 1950;33:23.\r\n2.\tChan A, Lakshminrusimha S, Heffner R, Gonzalez-Fernandez F. Histogenesis of retinal dysplasia in trisomy 13. Diagn Pathol. 2007;2:48.\r\n3.\tde Graaf P, van der Valk P, Moll AC, Imhof SM, Schouten-van Meeteren AY, Castelijns JA. Retinal dysplasia mimicking intraocular tumor: MR imaging findings with histopathologic correlation. AJNR Am J Neuroradiol.2007;28(9):1731-1733.\r\n4.\tLloyd IC, Colley A, Tullo AB, Bonshek R. Dominantly inherited unilateral retinal dysplasia. Br J Ophthalmol. 1993;77(6):378-80.\r\n5.\tAgarwal N, Gupta P, Agarwal A, Pantola C. Retinal Dysplasia – A Mimic of Malignant Ocular Pathology. J of Clinical and Diagnostic Research. 2011:5(2);367-368.\r\n6.\tGonzalez-Fernandez F, Lopes MB, Garcia-Fernandez JM, Foster RG, De Grip WJ, Rosemberg S, Newman SA, VandenBerg SR. Expression of developmentally defined retinal phenotypes in the histogenesis of retinoblastoma. Am J Pathol. 1992;141(2):363-375.\r\n7.\tEagle EC. Ch 11, Retinoblastoma and other pediatric intraocular tumors. In Eye Pathology – An Atlas and Basic Text. W.B. Saunders Co., Philadelphia. 1999. p. 199-205."
relation_type: []
relation_uri: []
reportno: ~
rev_number: 9
series: ~
source: ~
status_changed: 2013-05-04 23:08:39
subjects:
- OJHAS
succeeds: ~
suggestions: ~
sword_depositor: ~
sword_slug: ~
thesistype: ~
title: Retinal Dysplasia Mimicking Retinoblastoma.
type: journale
userid: 4338
volume: 11