---
abstract: 'Aggressive angiomyxoma(AA) is defined as benign neoplasm but has infiltrative potential into skeletal muscle and fat. Aggressive angiomyxoma is a rare neoplasm with about 150 reported cases so far. It is most often found in women in reproductive age with a peak incidence in the fourth decade of life. Aggressive angiomyxoma is most often found in or in proximity to the lower pelvis, more specifically perineum, vulva, vagina or inguinal regions. Most AA are big, often more than 10 cm in largest diameter. Radical surgery with wide margins is the treatment of choice. The prognosis is very good here. Because of its rarity and unique presentation we are reporting a case of a huge perineal AA in a 42 years female which presented as a tumour coming out of the breach in skin. She underwent surgery, wide local excision and after 7 months follow-up is free of tumor. '
altloc:
  - http://www.ojhas.org/issue45/2013-1-11.html
chapter: ~
commentary: ~
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creators_id:
  - ravi2varsha@yahoo.co.in
  - ~
  - ~
creators_name:
  - family: Patil
    given: RN
    honourific: ''
    lineage: ''
  - family: Reshme
    given: N
    honourific: ''
    lineage: ''
  - family: Kundargi
    given: R
    honourific: ''
    lineage: ''
date: 2013-04-15
date_type: published
datestamp: 2014-02-25 12:41:09
department: ~
dir: disk0/00/00/91/45
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editors_id:
  - Kakkilaya BS
editors_name:
  - family: Kakkilaya
    given: Srinivas
    honourific: Dr
    lineage: ''
eprint_status: archive
eprintid: 9145
fileinfo: /style/images/fileicons/application_pdf.png;/9145/1/2013-1-11.pdf
full_text_status: public
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keywords: Aggressive angiomyxoma; Vulva; Benign; Surgery
lastmod: 2014-02-25 12:41:09
latitude: ~
longitude: ~
metadata_visibility: show
note: ~
number: 1(11)
pagerange: ~
pubdom: TRUE
publication: Online Journal of Health and Allied Sciences
publisher: Kakkilaya BS
refereed: TRUE
referencetext: "1.\tMicci F, Brandal P . Soft Tissue Tumors: Aggressive angiomyxoma. Atlas Genet Cytogenet Oncol Haematol. April 2007;11(4)340-343. Available at http://documents.irevues.inist.fr/bitstream/handle/2042/16967/04-2007-AggresAngiomyxomaID5203.pdf.\r\n2.\tKempson RL, Teixeira MR, Hendrickson MR. Tumors of the Vulva - Mesenchymal tumours. In: Travasolli F A, Devilee P. (Eds). World Health Organization Classification of Tumors - Pathology and Genetics of Tumours of the Breast and Female Genital Organs. IARC Press; Lyon. 2003. pages 328-329. Available at http://www.iarc.fr/en/publications/pdfs-online/pat-gen/bb4/bb4-chap7.pdf.\r\n3.\tCoppola S, Desai A, Tzania D et al. Conservative En Bloc Surgery for Aggressive Angiomyxoma Achieves Good Local Control: Analysis of 14 Patients From a Single Institution. Int Journ of Gynecol Cancer. 2013;23:540-545.\r\n4.\tBehranwala KA, Thomas JM. 'Aggressive' angiomyxoma: a distinct clinical entity. Eur J Surg Oncol. 2003;29(7):559-563.\r\n5.\tSadaghiani MM, Nazari F, Atashkhoei S. Aggressive Angiomyxoma of the Vulva: a Case Report. Shiraz E-Medical Journal. 2009;10(4):231-235.\r\n6.\tSteeper TA, Rosai J. Aggressive angiomyxoma of the pelvis and perineum: report of nine cases of a distinctive type of gynaecologic soft tissue neoplasm. Am J Clin Pathol. 1983;7:463-475."
relation_type: []
relation_uri: []
reportno: ~
rev_number: 8
series: ~
source: ~
status_changed: 2014-02-25 12:41:09
subjects:
  - OJHAS
succeeds: ~
suggestions: ~
sword_depositor: ~
sword_slug: ~
thesistype: ~
title: 'Perineal Aggressive Angiomyxoma: A Rare Presentation'
type: journale
userid: 4338
volume: 12
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