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Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia

Indik, Julia H. and Marcus, Frank I. (2003) Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia. [Journal (Paginated)]

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Abstract

Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is characterized by the patchy replacement of myocardium by fatty or fibrofatty tissue. These changes lead to structural abnormalities including right ventricular enlargement and wall motion abnormalities that can be detected by echocardiography, angiography, and cine MRI. ARVC/D is a genetically heterogeneous disorder, since it has been linked to several chromosomal loci. Myocarditis may also be a contributing etiological factor. Patients are typically diagnosed during adolescence or young adulthood. Presenting symptoms are generally related to ventricular arrhythmias. Concern for the risk of sudden cardiac death may lead to the implantation of an intracardiac defibrillator. An ongoing multicenter international registry should further our understanding of this disease.

Item Type:Journal (Paginated)
Keywords:Arrhythmogenic right ventricular cardiomyopathy
Subjects:JOURNALS > Indian Pacing and Electrophysiology Journal
ID Code:4279
Deposited By: Indian Pacing and Electrophysiology, Journal
Deposited On:24 Apr 2005
Last Modified:11 Mar 2011 08:55

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